These Highlights Do Not Include All The Information Needed To Use Orenitram Safely And Effectively. See Full Prescribing Information For Orenitram.

These Highlights Do Not Include All The Information Needed To Use Orenitram Safely And Effectively. See Full Prescribing Information For Orenitram.
SPL v24
SPL
SPL Set ID 8ed2003a-c801-411e-831e-d06079bb0d7c
Route
ORAL
Published
Effective Date 2023-08-09
Document Type 34391-3 HUMAN PRESCRIPTION DRUG LABEL

Drug Facts

Composition & Product

Active Ingredients
Treprostinil (0.125 mg)
Inactive Ingredients
Xylitol Maltodextrin Sodium Lauryl Sulfate Magnesium Stearate Cellulose Acetate Triethyl Citrate Polyvinyl Alcohol, Unspecified Titanium Dioxide Polyethylene Glycol 3350 Talc Shellac Ferrosoferric Oxide Butyl Alcohol Alcohol Isopropyl Alcohol Propylene Glycol Fd&c Blue No. 2 Ferric Oxide Yellow Ferric Oxide Red

Identifiers & Packaging

Pill Appearance
Imprint: UT;1 Shape: round Color: white Color: green Color: yellow Color: pink Color: red Size: 8 mm Score: 1
Marketing Status
NDA Active Since 2023-02-14 Until 2024-02-29

Description

Dosage and Administration ( 2.1 ) 08/2023

Indications and Usage

Orenitram is a prostacyclin mimetic indicated for the treatment of pulmonary arterial hypertension (PAH) (WHO Group 1): To delay disease progression and to improve exercise capacity. The studies that established effectiveness included predominately patients with WHO functional class II-III symptoms and etiologies of idiopathic or heritable PAH (66%) or PAH associated with connective tissue disease (26%). ( 1.1 )

Dosage and Administration

Give with food. Swallow tablets whole; use only intact tablets. ( 2.1 ) Starting dose: 0.125 mg TID or 0.25 mg BID. ( 2.1 ) Titrate by 0.125 mg TID or by 0.25 mg or 0.5 mg BID, not more frequently than every 3 to 4 days as tolerated. The maximum daily dose is 120 mg. ( 2.1 ) If transitioning from intravenous (IV) or subcutaneous (SC) Remodulin ® , the Orenitram dose should be increased while simultaneously decreasing the IV/SC infusion rate. ( 2.2 ) Mild hepatic impairment (Child Pugh Class A): Initiate at 0.125 mg BID. Increment at 0.125 mg BID not more frequently than every 3 to 4 days. ( 2.3 ) Avoid use in patients with moderate hepatic impairment. ( 2.3 )

Warnings and Precautions

Do not abruptly discontinue dosing. ( 2.5 , 5.1 ) In patients with diverticulosis, Orenitram tablets can become lodged in a diverticulum. ( 5.2 )

Contraindications

Severe hepatic impairment (Child Pugh Class C) [see Use In Specific Populations (8.6) and Clinical Pharmacology (12.3) ] .

Adverse Reactions

Most common adverse reactions (incidence >10%) reported in clinical studies in patients treated with Orenitram compared with placebo are headache, diarrhea, nausea, vomiting, jaw pain, and flushing. ( 6.1 ) To report SUSPECTED ADVERSE REACTIONS, contact United Therapeutics Corp. at 1-866-458-6479 or FDA at 1-800-FDA-1088 or www.fda.gov/medwatch.

Drug Interactions

When co-administered with strong CYP2C8 inhibitors the initial dose is 0.125 mg BID with 0.125 mg BID dose increments not more frequently than every 3 to 4 days. ( 2.4 , 7.1 )

How Supplied

Orenitram is an 8-mm round biconvex tablet with strength identified by color and print and supplied as follows: Strength Color Printing on Tablets NDC # 100-Count Bottle NDC # 10-Count Bottle NDC # 10-Count Carton (Unit-Dose Blister) 0.125 mg White UT 0.125 66302-300-01 66302-300-10 66302-300-02 0.25 mg Green UT 0.25 66302-302-01 66302-302-10 66302-302-02 1 mg Yellow UT 1 66302-310-01 66302-310-10 66302-310-02 2.5 mg Pink UT 2.5 66302-325-01 66302-325-10 66302-325-02 5 mg Red UT 5 66302-350-01 66302-350-10 66302-350-02 Titration Kits for Orenitram are supplied in the following configurations: Titration Kit Blister Configurations NDC # Month 1 containing four weekly cartons Seven daily wallet blister packs in each weekly carton containing the following total number of tablets: Week 1 (twenty-one × 0.125 mg tablets) Week 2 (forty-two × 0.125 mg tablets) Week 3 (twenty-one × 0.125 mg tablets and twenty-one × 0.25 mg tablets) Week 4 (forty-two × 0.125 mg tablets and twenty-one × 0.25 mg tablets) 66302-361-28 Month 2 containing four weekly cartons Seven daily wallet blister packs in each weekly carton containing the following total number of tablets: Week 5 (twenty-one × 0.125 mg tablets and forty-two × 0.25 mg tablets) Week 6 (forty-two × 0.125 mg tablets and forty-two × 0.25 mg tablets) Week 7 (twenty-one × 0.125 mg tablets and sixty-three × 0.25 mg tablets) Week 8 (forty-two × 0.125 mg tablets and sixty-three × 0.25 mg tablets) 66302-362-56 Month 3 containing four weekly cartons Seven daily wallet blister packs in each weekly carton containing the following total number of tablets: Week 9 (twenty-one × 0.125 mg tablets and twenty-one × 1 mg tablets) Week 10 (forty-two × 0.125 mg tablets and twenty-one × 1 mg tablets) Week 11 (twenty-one × 0.125 mg tablets, twenty-one × 0.25 mg tablets, and twenty-one × 1 mg tablets) Week 12 (forty-two × 0.125 mg tablets, twenty-one × 0.25 mg tablets, and twenty-one × 1 mg tablets) 66302-363-84


Medication Information

Warnings and Precautions

Do not abruptly discontinue dosing. ( 2.5 , 5.1 ) In patients with diverticulosis, Orenitram tablets can become lodged in a diverticulum. ( 5.2 )

Indications and Usage

Orenitram is a prostacyclin mimetic indicated for the treatment of pulmonary arterial hypertension (PAH) (WHO Group 1): To delay disease progression and to improve exercise capacity. The studies that established effectiveness included predominately patients with WHO functional class II-III symptoms and etiologies of idiopathic or heritable PAH (66%) or PAH associated with connective tissue disease (26%). ( 1.1 )

Dosage and Administration

Give with food. Swallow tablets whole; use only intact tablets. ( 2.1 ) Starting dose: 0.125 mg TID or 0.25 mg BID. ( 2.1 ) Titrate by 0.125 mg TID or by 0.25 mg or 0.5 mg BID, not more frequently than every 3 to 4 days as tolerated. The maximum daily dose is 120 mg. ( 2.1 ) If transitioning from intravenous (IV) or subcutaneous (SC) Remodulin ® , the Orenitram dose should be increased while simultaneously decreasing the IV/SC infusion rate. ( 2.2 ) Mild hepatic impairment (Child Pugh Class A): Initiate at 0.125 mg BID. Increment at 0.125 mg BID not more frequently than every 3 to 4 days. ( 2.3 ) Avoid use in patients with moderate hepatic impairment. ( 2.3 )

Contraindications

Severe hepatic impairment (Child Pugh Class C) [see Use In Specific Populations (8.6) and Clinical Pharmacology (12.3) ] .

Adverse Reactions

Most common adverse reactions (incidence >10%) reported in clinical studies in patients treated with Orenitram compared with placebo are headache, diarrhea, nausea, vomiting, jaw pain, and flushing. ( 6.1 ) To report SUSPECTED ADVERSE REACTIONS, contact United Therapeutics Corp. at 1-866-458-6479 or FDA at 1-800-FDA-1088 or www.fda.gov/medwatch.

Drug Interactions

When co-administered with strong CYP2C8 inhibitors the initial dose is 0.125 mg BID with 0.125 mg BID dose increments not more frequently than every 3 to 4 days. ( 2.4 , 7.1 )

How Supplied

Orenitram is an 8-mm round biconvex tablet with strength identified by color and print and supplied as follows: Strength Color Printing on Tablets NDC # 100-Count Bottle NDC # 10-Count Bottle NDC # 10-Count Carton (Unit-Dose Blister) 0.125 mg White UT 0.125 66302-300-01 66302-300-10 66302-300-02 0.25 mg Green UT 0.25 66302-302-01 66302-302-10 66302-302-02 1 mg Yellow UT 1 66302-310-01 66302-310-10 66302-310-02 2.5 mg Pink UT 2.5 66302-325-01 66302-325-10 66302-325-02 5 mg Red UT 5 66302-350-01 66302-350-10 66302-350-02 Titration Kits for Orenitram are supplied in the following configurations: Titration Kit Blister Configurations NDC # Month 1 containing four weekly cartons Seven daily wallet blister packs in each weekly carton containing the following total number of tablets: Week 1 (twenty-one × 0.125 mg tablets) Week 2 (forty-two × 0.125 mg tablets) Week 3 (twenty-one × 0.125 mg tablets and twenty-one × 0.25 mg tablets) Week 4 (forty-two × 0.125 mg tablets and twenty-one × 0.25 mg tablets) 66302-361-28 Month 2 containing four weekly cartons Seven daily wallet blister packs in each weekly carton containing the following total number of tablets: Week 5 (twenty-one × 0.125 mg tablets and forty-two × 0.25 mg tablets) Week 6 (forty-two × 0.125 mg tablets and forty-two × 0.25 mg tablets) Week 7 (twenty-one × 0.125 mg tablets and sixty-three × 0.25 mg tablets) Week 8 (forty-two × 0.125 mg tablets and sixty-three × 0.25 mg tablets) 66302-362-56 Month 3 containing four weekly cartons Seven daily wallet blister packs in each weekly carton containing the following total number of tablets: Week 9 (twenty-one × 0.125 mg tablets and twenty-one × 1 mg tablets) Week 10 (forty-two × 0.125 mg tablets and twenty-one × 1 mg tablets) Week 11 (twenty-one × 0.125 mg tablets, twenty-one × 0.25 mg tablets, and twenty-one × 1 mg tablets) Week 12 (forty-two × 0.125 mg tablets, twenty-one × 0.25 mg tablets, and twenty-one × 1 mg tablets) 66302-363-84

Description

Dosage and Administration ( 2.1 ) 08/2023

Section 42229-5

Risk Summary

Limited published data from case reports with Orenitram use in pregnant women are not sufficient to assess for a drug-associated risk of major birth defects, miscarriage, or adverse maternal or fetal outcomes. There are risks to the mother and the fetus associated with pulmonary arterial hypertension (see Clinical Considerations). Animal reproductive studies with treprostinil diolamine administered orally have shown an adverse effect on the fetus. In rats, administration of treprostinil to pregnant rats during the period of organogenesis at doses ≥10 mg/kg/day (approximately 15 times the human exposure at the dose of 3.5 mg BID on an AUC basis) resulted in decreased pregnancy rate, increased post-implantation loss, and decreased fetal viability and growth. In rabbits, teratogenicity and decreased fetal viability and growth were observed at doses ≥1.5 mg/kg/day (approximately 7 times the human exposure at the dose of 3.5 mg BID on an AUC basis) (see Animal Data).

The estimated background risk of major birth defects and miscarriage for the indicated populations is unknown. All pregnancies have a background risk of birth defect, loss, or other adverse outcomes. In the U.S. general population, the estimated background risk of major birth defects and miscarriage in clinically recognized pregnancies is 2 to 4% and 15 to 20%, respectively.

Section 42230-3
This Patient Information has been approved by the U.S. Food and Drug Administration. Revised: 02/2023
Patient Information

Orenitram(®) (oh-REN-i-tram)

(treprostinil) extended-release tablets
What is Orenitram?
  • Orenitram is a prescription medicine used to treat pulmonary arterial hypertension (PAH) which is high blood pressure in the arteries of your lungs.
  • Orenitram can help slow down the progression of your disease and improve your ability to exercise.
It is not known if Orenitram is safe and effective in children.
Do not take Orenitram if you have severe liver problems.
Before taking Orenitram, tell your healthcare provider about all of your medical conditions, including if you:
  • have liver problems
  • have diverticulosis
  • are pregnant or plan to become pregnant. It is not known if Orenitram will harm your unborn baby.
  • are breastfeeding or plan to breastfeed. It is not known if Orenitram passes into your breast milk. Talk to your healthcare provider about the best way to feed your baby during treatment with Orenitram.
Tell your healthcare provider about all the medicines you take, including prescription and over-the-counter medicines, vitamins, and herbal supplements. Orenitram and other medicines may affect each other causing side effects. Do not start any new medicine until you check with your healthcare provider.

Especially tell your healthcare provider if you take another medicine that contains treprostinil, such as Remodulin®, Tyvaso®, or Tyvaso DPI®.
How should I take Orenitram?
  • Take Orenitram exactly as your healthcare provider tells you to take it.
  • Your healthcare provider will slowly increase your dose to find the dose of Orenitram that is right for you.
  • If you take the medicine Remodulin and your healthcare provider is switching you to Orenitram, your healthcare provider will decrease your dose of Remodulin over a period of time when you start taking Orenitram.
  • Do not change your dose or suddenly stop taking Orenitram without first talking to your healthcare provider.
  • Orenitram is usually taken 3 times a day (about every 8 hours) or 2 times a day (about every 12 hours). Your healthcare provider will tell you how often you should take Orenitram. If you have side effects, your healthcare provider may tell you to change your dose or when you take Orenitram.
  • Take Orenitram with food.
  • Swallow Orenitram tablets whole. Do not split, chew, crush, or break your Orenitram tablets. Do not take Orenitram tablets that are damaged or broken. If Orenitram tablets are not taken whole, they may release too much medicine at one time. This can lead to side effects.
  • You may see the tablet shell in your stools (bowel movements). This is usually normal. The tablet shell is not digested. If you have diverticulosis, the tablet shell may get stuck in a blind pouch or diverticulum in your intestine.
  • If you miss your dose of Orenitram, take the missed dose as soon as possible with food.
  • If you miss 2 or more doses of Orenitram, call your healthcare provider to see if you need to change your dose.
  • If you take too much Orenitram, call your healthcare provider or go to the nearest hospital emergency room right away.
What are the possible side effects of Orenitram?

Orenitram can cause serious side effects, including worsening of PAH symptoms.
  • Stopping Orenitram suddenly may cause worsening of your PAH symptoms. Do not change your dose or suddenly stop taking Orenitram without first talking to your healthcare provider.
The most common side effects of Orenitram include:
  • headache
  • diarrhea
  • nausea
  • vomiting
  • flushing
  • pain in arms and legs
  • jaw pain
Tell your healthcare provider if you have any side effect that bothers you or that does not go away.

These are not all of the possible side effects of Orenitram. For more information, ask your healthcare provider or pharmacist.

Call your healthcare provider for medical advice about side effects. You may report side effects to FDA at 1-800-FDA-1088.
How should I store Orenitram?
  • Store at 68°F to 77°F (20°C to 25°C).
Keep Orenitram and all medicines out of the reach of children.
General information about the safe and effective use of Orenitram.

Medicines are sometimes prescribed for purposes other than those listed in a Patient Information Leaflet.

Do not use Orenitram for a condition for which it was not prescribed. Do not give Orenitram to other people, even if they have the same symptoms that you have. It may harm them. You can ask your healthcare provider or pharmacist for information about Orenitram that is written for health professionals.
What are the ingredients in Orenitram?

Active ingredient: treprostinil diolamine

Inactive ingredients: xylitol, maltodextrin, sodium lauryl sulfate, magnesium stearate, cellulose acetate, triethyl citrate, polyvinyl alcohol, titanium dioxide, polyethylene glycol, and talc. In addition, tablets may contain colorants FD&C Blue #2, iron oxide yellow, and iron oxide red. The imprint ink contains shellac glaze, ethanol, isopropyl alcohol, iron oxide black, n-butyl alcohol, and propylene glycol.

United Therapeutics Corp., Research Triangle Park, NC 27709 USA

Copyright 2023, United Therapeutics Corp. All rights reserved.

ORENITRAM is a registered trademark of United Therapeutics Corp.

For more information, go to www.orenitram.com or call 1-877-864-8437.
Section 43683-2
Dosage and Administration (2.1) 08/2023
16.2 Storage

Store at 20°C to 25°C (68°F to 77°F) with excursions permitted to 15°C to 30°C (59°F to 86°F) [See USP Controlled Room Temperature]. Keep out of reach of children.

10 Overdosage

Signs and symptoms of overdose with Orenitram during clinical trials reflect its dose-limiting pharmacologic effects and include severe headache, nausea, vomiting, diarrhea, and hypotension. Treat supportively.

11 Description

Orenitram is an extended-release osmotic tablet for oral administration. Orenitram is formulated as the diolamine salt of treprostinil, a tricyclic benzindene analogue of prostacyclin. The chemical name is Acetic acid, 2-[[(1R,2R,3aS,9aS)-2,3,3a,4,9,9a-hexahydro-2-hydroxy-1-[(3S)-3-hydroxyoctyl]-1H-benz[f]inden-5-yl]oxy]-, complexed with 2,2'-iminobis[ethanol] (1:1). The molecular formula is C23H34O5∙C4H11NO2, the molecular weight is 495.65, and it has the following structural formula:

Orenitram tablets are formulated in five strengths, which contain 0.125 mg of treprostinil (equivalent to 0.159 mg treprostinil diolamine), 0.25 mg of treprostinil (equivalent to 0.317 mg treprostinil diolamine), 1 mg of treprostinil (equivalent to 1.27 mg treprostinil diolamine), 2.5 mg of treprostinil (equivalent to 3.17 mg treprostinil diolamine), or 5 mg of treprostinil (equivalent to 6.35 mg treprostinil diolamine). The formulations also contain xylitol, maltodextrin, sodium lauryl sulfate, magnesium stearate, cellulose acetate, triethyl citrate, polyvinyl alcohol, titanium dioxide, polyethylene glycol, and talc. In addition, tablets may contain colorants FD&C Blue #2, iron oxide yellow, and iron oxide red. The imprint ink contains shellac glaze, ethanol, isopropyl alcohol USP, iron oxide black, n-butyl alcohol, and propylene glycol.

Orenitram is designed to release treprostinil at a near zero-order rate using an osmotic tablet technology. The tablet core is coated with a semi-permeable membrane and has a laser-drilled aperture through the membrane. Upon contact with water (e.g., after ingestion), the core tablet absorbs water through the semi-permeable membrane. The water dissolves the water-soluble treprostinil diolamine and the water-soluble osmotic excipients, which creates hydrostatic pressure within the membrane, eventually forcing the drug across the membrane at a controlled rate.

16.1 How Supplied

Orenitram is an 8-mm round biconvex tablet with strength identified by color and print and supplied as follows:

Strength Color Printing on Tablets NDC #

100-Count Bottle
NDC #

10-Count Bottle
NDC #

10-Count Carton (Unit-Dose Blister)
0.125 mg White UT 0.125 66302-300-01 66302-300-10 66302-300-02
0.25 mg Green UT 0.25 66302-302-01 66302-302-10 66302-302-02
1 mg Yellow UT 1 66302-310-01 66302-310-10 66302-310-02
2.5 mg Pink UT 2.5 66302-325-01 66302-325-10 66302-325-02
5 mg Red UT 5 66302-350-01 66302-350-10 66302-350-02

Titration Kits for Orenitram are supplied in the following configurations:

Titration Kit Blister Configurations NDC #
Month 1 containing four weekly cartons Seven daily wallet blister packs in each weekly carton containing the following total number of tablets:
  • Week 1 (twenty-one × 0.125 mg tablets)
  • Week 2 (forty-two × 0.125 mg tablets)
  • Week 3 (twenty-one × 0.125 mg tablets and twenty-one × 0.25 mg tablets)
  • Week 4 (forty-two × 0.125 mg tablets and twenty-one × 0.25 mg tablets)
66302-361-28
Month 2 containing four weekly cartons Seven daily wallet blister packs in each weekly carton containing the following total number of tablets:
  • Week 5 (twenty-one × 0.125 mg tablets and forty-two × 0.25 mg tablets)
  • Week 6 (forty-two × 0.125 mg tablets and forty-two × 0.25 mg tablets)
  • Week 7 (twenty-one × 0.125 mg tablets and sixty-three × 0.25 mg tablets)
  • Week 8 (forty-two × 0.125 mg tablets and sixty-three × 0.25 mg tablets)
66302-362-56
Month 3 containing four weekly cartons Seven daily wallet blister packs in each weekly carton containing the following total number of tablets:
  • Week 9 (twenty-one × 0.125 mg tablets and twenty-one × 1 mg tablets)
  • Week 10 (forty-two × 0.125 mg tablets and twenty-one × 1 mg tablets)
  • Week 11 (twenty-one × 0.125 mg tablets, twenty-one × 0.25 mg tablets, and twenty-one × 1 mg tablets)
  • Week 12 (forty-two × 0.125 mg tablets, twenty-one × 0.25 mg tablets, and twenty-one × 1 mg tablets)
66302-363-84
8.4 Pediatric Use

Safety and effectiveness in pediatric patients have not been established.

8.5 Geriatric Use

Use of Orenitram in patients aged 65 years and over demonstrated slightly higher absolute and relative adverse event rates compared to younger patients. In general, dose selection for an elderly patient should be cautious, reflecting the greater frequency of decreased hepatic or cardiac function, and of concomitant disease or other drug therapy.

4 Contraindications

Severe hepatic impairment (Child Pugh Class C) [see Use In Specific Populations (8.6) and Clinical Pharmacology (12.3)].

6 Adverse Reactions

Most common adverse reactions (incidence >10%) reported in clinical studies in patients treated with Orenitram compared with placebo are headache, diarrhea, nausea, vomiting, jaw pain, and flushing. (6.1)



To report SUSPECTED ADVERSE REACTIONS, contact United Therapeutics Corp. at 1-866-458-6479 or FDA at 1-800-FDA-1088 or www.fda.gov/medwatch.

7 Drug Interactions
  • When co-administered with strong CYP2C8 inhibitors the initial dose is 0.125 mg BID with 0.125 mg BID dose increments not more frequently than every 3 to 4 days. (2.4, 7.1)
12.2 Pharmacodynamics

In a clinical trial of 240 healthy adult volunteers, single doses of inhaled treprostinil 54 µg (the target clinical dose) and 84 µg (supratherapeutic inhalation dose) prolonged the corrected QTc interval by approximately 10 msec. The QTc effect dissipated rapidly as the concentration of treprostinil decreased. Orenitram has not been evaluated in a thorough QTc study.

12.3 Pharmacokinetics

In patients with PAH, pharmacokinetics of treprostinil is dose-proportional for systemic exposure (AUC0-t) over the dose range from 0.5 to 15 mg BID. Upon repeat administration with a BID regimen, the accumulation in the systemic exposures to treprostinil is minimal and results in a peak-to-trough ratio of approximately 7. However, a TID regimen will reduce the peak-to-trough fluctuations to approximately 2.5 for the same total daily dose.

2.1 Recommended Dosing

Take Orenitram with food. Swallow Orenitram tablets whole; do not crush, split, or chew.

The recommended starting dose of Orenitram is 0.125 mg three times daily (TID) with food, taken approximately 8 hours apart or 0.25 mg twice daily (BID) with food, taken approximately 12 hours apart.

Titrate by 0.125 mg TID or 0.25 or 0.5 mg BID not more frequently than every 3 to 4 days. Increase the dose to the highest tolerated dose. The recommended maximum daily dose is 120 mg.

If dose increments are not tolerated, consider titrating slower. If intolerable pharmacologic effects occur, decrease the dose in increments of 0.125 mg TID or 0.25 mg BID. Avoid abrupt discontinuation [see Warnings and Precautions (5.1)].

1 Indications and Usage

Orenitram is a prostacyclin mimetic indicated for the treatment of pulmonary arterial hypertension (PAH) (WHO Group 1):

  • To delay disease progression and to improve exercise capacity. The studies that established effectiveness included predominately patients with WHO functional class II-III symptoms and etiologies of idiopathic or heritable PAH (66%) or PAH associated with connective tissue disease (26%). (1.1)
12.1 Mechanism of Action

The major pharmacologic actions of treprostinil are direct vasodilation of pulmonary and systemic arterial vascular beds, inhibition of platelet aggregation, and inhibition of smooth muscle cell proliferation.

5 Warnings and Precautions
  • Do not abruptly discontinue dosing. (2.5, 5.1)
  • In patients with diverticulosis, Orenitram tablets can become lodged in a diverticulum. (5.2)
2 Dosage and Administration
  • Give with food. Swallow tablets whole; use only intact tablets. (2.1)
  • Starting dose: 0.125 mg TID or 0.25 mg BID. (2.1)
  • Titrate by 0.125 mg TID or by 0.25 mg or 0.5 mg BID, not more frequently than every 3 to 4 days as tolerated. The maximum daily dose is 120 mg. (2.1)
  • If transitioning from intravenous (IV) or subcutaneous (SC) Remodulin®, the Orenitram dose should be increased while simultaneously decreasing the IV/SC infusion rate. (2.2)
  • Mild hepatic impairment (Child Pugh Class A): Initiate at 0.125 mg BID. Increment at 0.125 mg BID not more frequently than every 3 to 4 days. (2.3)
  • Avoid use in patients with moderate hepatic impairment. (2.3)
3 Dosage Forms and Strengths

Orenitram (treprostinil) extended-release tablets are available in the following five strengths:

  • -
    0.125 mg [White tablet imprinted with UT 0.125]
  • -
    0.25 mg [Green tablet imprinted with UT 0.25]
  • -
    1 mg [Yellow tablet imprinted with UT 1]
  • -
    2.5 mg [Pink tablet imprinted with UT 2.5]
  • -
    5 mg [Red tablet imprinted with UT 5]
6.2 Post Marketing Experience

The following adverse reactions have been identified during postapproval use of Orenitram: dizziness, dyspepsia, vomiting, myalgia, and arthralgia. Because these reactions are reported voluntarily from a population of uncertain size, it is not always possible to reliably estimate their frequency or establish a causal relationship to drug exposure.

6.1 Clinical Trials Experience

Because clinical trials are conducted under widely varying conditions, adverse reaction rates observed in the clinical trials of a drug cannot be directly compared to rates in the clinical trials of another drug and may not reflect the rates observed in clinical practice.

In a 12-week, placebo-controlled, monotherapy study (Study 1; WHO Group 1; functional class II-III), and an event-driven, placebo-controlled, combination therapy study (Study 4; WHO Group 1; functional class I-III), the most commonly reported adverse reactions that occurred in patients receiving Orenitram included: headache, diarrhea, nausea, and flushing.

Orenitram patients in Study 1 (N=151) had access to 0.25 mg tablets at randomization. Approximately 91% of such patients in Study 1 experienced an adverse reaction, but only 4% discontinued therapy for an adverse reaction (compared to 3% receiving placebo). Study 4 enrolled a total of 690 patients, 346 received Orenitram and 344 received placebo. Overall, 19% of patients treated with Orenitram discontinued treatment in Study 4 due to an adverse event (compared to 4% of patients receiving placebo). The exposure to Orenitram in Study 4 was up to 5.1 years with a median duration of exposure of 1.2 years. Table 1 summarizes adverse events with rates at least 5% higher on Orenitram therapy than on placebo that were reported in either Study 1 or 4.

Table 1: Adverse Events with Rates at Least 5% Higher on Orenitram Therapy than on Placebo in Either Study 1 or Study 4
Reaction Study 1

N=228
Includes all subjects in the Primary Analysis Population
Study 4

N=690
Orenitram

n=151
Placebo

n=77
Orenitram

n=346
Placebo

n=344
Headache 63% 19% 75% 35%
Diarrhea 30% 16% 69% 29%
Nausea 30% 18% 40% 23%
Vomiting 17% 16% 36% 10%
Flushing 15% 6% 45% 8%
Pain in jaw 11% 4% 18% 3%
Pain in extremity 14% 8% 18% 9%
Hypokalemia 9% 3% 4% 3%
Abdominal discomfort 6% 0% 8% 4%
Upper abdominal pain 5% 3% 12% 5%

Orenitram was studied in a long-term, open-label, extension study in which 824 patients were dosed for a mean duration of approximately 2 years. About 70% of patients continued treatment with Orenitram for at least a year. The mean dose was 4.2 mg BID at one year. The adverse reactions were similar to those observed in the placebo-controlled trials.

The safety of Orenitram was also evaluated in an open-label study transitioning patients from Remodulin. The safety profile during this study was similar to that observed in the three pivotal studies.

17 Patient Counseling Information

See FDA-approved patient labeling (Patient Information).

Tell patients:

  • Abrupt discontinuation of therapy could result in worsening of PAH symptoms.
  • Take Orenitram with food.
  • Swallow Orenitram tablets whole. Do not split, chew, crush, or break. Do not take a tablet that is damaged or broken.
  • The biologically inert components of the tablet remain intact during gastrointestinal transit and are eliminated in the feces as an insoluble shell.
8.7 Patients With Renal Impairment

No dose adjustments are required in patients with renal impairment. Orenitram is not removed by dialysis [see Clinical Pharmacology (12.3)].

1.1 Pulmonary Arterial Hypertension

Orenitram is indicated for the treatment of pulmonary arterial hypertension (PAH) (WHO Group 1) to delay disease progression and to improve exercise capacity.

The studies that established effectiveness included predominately patients with WHO functional class II-III symptoms and etiologies of idiopathic or heritable PAH (66%) or PAH associated with connective tissue disease (26%).

8.6 Patients With Hepatic Impairment

There is a marked increase in the systemic exposure to treprostinil in hepatically impaired patients [see Dosage and Administration (2.3), Contraindications (4), and Clinical Pharmacology (12.3)].

2.5 Interruptions and Discontinuation

If a dose of medication is missed, the patient should take the missed dose as soon as possible, with food. If a patient misses two or more doses, restart at a lower dose and re-titrate.

In the event of a planned short-term treatment interruption for patients unable to take oral medications, consider a temporary infusion of subcutaneous or intravenous treprostinil. To calculate the total daily dose (mg) of treprostinil for the parenteral route use the following equation:

Remodulin (ng/kg/min) = 139 × Orenitram total daily dose (mg)
                      weight (kg)

When discontinuing Orenitram, reduce the dose in steps of 0.5 to 1 mg per day [see Warnings and Precautions (5.1)].

5.2 Use in Patients With Blind End Pouches

The tablet shell does not dissolve. In patients with diverticulosis, Orenitram tablets can lodge in a diverticulum.

7.1 Effect of Cyp2c8 Inhibitors On Treprostinil

Co-administration of Orenitram and the CYP2C8 enzyme inhibitor gemfibrozil in healthy adult volunteers increases exposure to treprostinil. Reduce the starting dose of Orenitram to 0.125 mg BID and use 0.125 mg BID increments not more frequently than every 3 to 4 days [see Dosage and Administration (2.4) and Clinical Pharmacology (12.3)].

5.1 Worsening Pah Symptoms Upon Abrupt Withdrawal

Abrupt discontinuation or sudden large reductions in dosage of Orenitram may result in worsening of PAH symptoms.

2.4 Dose Adjustment for Use With Cyp2c8 Inhibitors

When co-administered with strong CYP2C8 inhibitors (e.g., gemfibrozil) the initial dose is 0.125 mg BID with 0.125 mg BID dose increments not more frequently than every 3 to 4 days.

Principal Display Panel 1 Mg Tablet Bottle Label

NDC 66302-310-01

100 Tablets

Orenitram®

(treprostinil)

Extended-Release

Tablets

1 mg

Swallow whole.

Do not split, chew, crush,

or break tablets.

Principal Display Panel 5 Mg Tablet Bottle Label

NDC 66302-350-01

100 Tablets

Orenitram®

(treprostinil)

Extended-Release

Tablets

5 mg

Swallow whole.

Do not split, chew, crush,

or break tablets.

Principal Display Panel 2.5 Mg Tablet Bottle Label

NDC 66302-325-01

100 Tablets

Orenitram®

(treprostinil)

Extended-Release

Tablets

2.5 mg

Swallow whole.

Do not split, chew, crush,

or break tablets.

Principal Display Panel 0.25 Mg Tablet Bottle Label

NDC 66302-302-01

100 Tablets

Orenitram®

(treprostinil)

Extended-Release

Tablets

0.25 mg

Swallow whole.

Do not split, chew, crush,

or break tablets.

Principal Display Panel 0.125 Mg Tablet Bottle Label

NDC 66302-300-01

100 Tablets

Orenitram®

(treprostinil)

Extended-Release

Tablets

0.125 mg

Swallow whole.

Do not split, chew, crush,

or break tablets.

14.1 Clinical Trials in Pulmonary Arterial Hypertension

Four multicenter, randomized, double-blind studies were conducted and compared Orenitram to placebo in a total of 349 (Study 1), 350 (Study 2), 310 (Study 3), and 690 (Study 4) patients with PAH.

2.3 Dose Adjustment in Patients With Hepatic Impairment

In patients with mild hepatic impairment (Child Pugh Class A) start at 0.125 mg BID with 0.125 mg BID dose increments not more frequently than every 3 to 4 days. Avoid use of Orenitram in patients with moderate hepatic impairment (Child Pugh Class B). Orenitram is contraindicated in patients with severe hepatic impairment (Child Pugh Class C) due to increases in systemic exposure [see Contraindications (4), Use in Specific Populations (8.6), and Clinical Pharmacology (12.3)].

13.1 Carcinogenesis, Mutagenesis, Impairment of Fertility

Treprostinil diolamine did not demonstrate any carcinogenic effects in mouse or rat carcinogenicity studies. Oral administration of treprostinil diolamine to Tg.rasH2 mice at 0, 5, 10, and 20 mg/kg/day in males and 0, 3, 7.5, and 15 mg/kg/day in females daily for 26 weeks did not significantly increase the incidence of tumors. Oral administration of treprostinil diolamine to Sprague Dawley rats at 0, 1, 3, and 10 mg/kg/day daily for 104 weeks did not significantly increase the incidence of tumors. The exposures obtained at the highest dose levels used in males and females are about 13- and 18-fold, respectively, the human exposure at the dose of 3.5 mg BID on an AUC basis.

In vitro genotoxicity studies with high doses of treprostinil did not demonstrate any mutagenic or clastogenic effects. Treprostinil diolamine was tested in vivo in a rat micronucleus assay and did not induce an increased incidence of micronucleated polychromatic erythrocytes.

In rats, treatment with treprostinil diolamine had no effect on reproductive performance or sperm motility at doses up to 10 mg/kg/day. The exposures at this dose level are about 6- (male) to 11- (female) fold the human exposure at the dose of 3.5 mg BID on an AUC basis.

Principal Display Panel 1 Mg Tablet Blister Pack Carton

Orenitram®

(treprostinil)

EXTENDED-RELEASE TABLETS

1 mg

per tablet

Swallow whole.

Do not split, chew,

crush, or break tablets.

10 Tablets

(1 x 10 tablet blister pack)

Pharmacist:

Dispense the accompanying Patient

Information Leaflet to each patient.

Rx Only

NDC 66302-310-02

Principal Display Panel 5 Mg Tablet Blister Pack Carton

Orenitram®

(treprostinil)

EXTENDED-RELEASE TABLETS

5 mg

per tablet

Swallow whole.

Do not split, chew,

crush, or break tablets.

10 Tablets

(1 x 10 tablet blister pack)

Pharmacist:

Dispense the accompanying Patient

Information Leaflet to each patient.

Rx Only

NDC 66302-350-02

Principal Display Panel 2.5 Mg Tablet Blister Pack Carton

Orenitram®

(treprostinil)

EXTENDED-RELEASE TABLETS

2.5 mg

per tablet

Swallow whole.

Do not split, chew,

crush, or break tablets.

10 Tablets

(1 x 10 tablet blister pack)

Pharmacist:

Dispense the accompanying Patient

Information Leaflet to each patient.

Rx Only

NDC 66302-325-02

Principal Display Panel 0.25 Mg Tablet Blister Pack Carton

Orenitram®

(treprostinil)

EXTENDED-RELEASE TABLETS

0.25 mg

per tablet

Swallow whole.

Do not split, chew,

crush, or break tablets.

10 Tablets

(1 x 10 tablet blister pack)

Pharmacist:

Dispense the accompanying Patient

Information Leaflet to each patient.

Rx Only

NDC 66302-302-02

Principal Display Panel 0.125 Mg Tablet Blister Pack Carton

Orenitram®

(treprostinil)

EXTENDED-RELEASE TABLETS

0.125 mg

per tablet

Swallow whole.

Do not split, chew,

crush, or break tablets.

10 Tablets

(1 x 10 tablet blister pack)

Pharmacist:

Dispense the accompanying Patient

Information Leaflet to each patient.

Rx Only

NDC 66302-300-02

Principal Display Panel 0.125 Mg 0.25 Mg Titration Kit Carton Month 1

Rx Only

NDC 66302-361-28

Orenitram®

(treprostinil)

EXTENDED-RELEASE TABLETS

Titration Kit

Month 1

0.125 mg

per tablet

0.25 mg

per tablet

Swallow whole.

Do not split, chew, crush, or break tablets.

Kit Contains:

168 tablets (126 x 0.125 mg per tablet and

42 x 0.25 mg per tablet).

Monthly carton contains 4 individual weekly cartons

each with 7 daily wallet blister packs.

Principal Display Panel 0.125 Mg 0.25 Mg Titration Kit Carton Month 2

Rx Only

NDC 66302-362-56

Orenitram®

(treprostinil)

EXTENDED-RELEASE TABLETS

Titration Kit

Month 2

0.125 mg

per tablet

0.25 mg

per tablet

Swallow whole.

Do not split, chew, crush, or break tablets.

Kit Contains:

336 tablets (126 x 0.125 mg per tablet and

210 x 0.25 mg per tablet).

Monthly carton contains 4 individual weekly cartons

each with 7 daily wallet blister packs.

Principal Display Panel 0.125 Mg 0.25 Mg 1 Mg Titration Kit Carton Month 3

Rx Only

NDC 66302-363-84

Orenitram®

(treprostinil)

EXTENDED-RELEASE TABLETS

Titration Kit

Month 3

0.125 mg

per tablet

0.25 mg

per tablet

1 mg

per tablet

Swallow whole.

Do not split, chew, crush, or break tablets.

Kit Contains:

252 tablets (126 x 0.125 mg per tablet,

42 x 0.25 mg per tablet, and 84 × 1 mg per tablet).

Monthly carton contains 4 individual weekly cartons

each with 7 daily wallet blister packs.

2.2 Transitioning From Subcutaneous Or Intravenous Routes of Administration of Treprostinil

Decrease the dose of Remodulin while simultaneously increasing the dose of Orenitram. The dose of Remodulin can be reduced up to 30 ng/kg/min per day and the dose of Orenitram simultaneously increased up to 6 mg per day (2 mg TID) if tolerated. The following equation can be used to estimate a target total daily dose of Orenitram in mg using a patient's dose of intravenous (IV)/subcutaneous (SC) treprostinil (in ng/kg/min) and weight (in kg).

Orenitram total daily dose (mg) = 0.0072 × Remodulin dose (ng/kg/min) × weight (kg)


Structured Label Content

Section 42229-5 (42229-5)

Risk Summary

Limited published data from case reports with Orenitram use in pregnant women are not sufficient to assess for a drug-associated risk of major birth defects, miscarriage, or adverse maternal or fetal outcomes. There are risks to the mother and the fetus associated with pulmonary arterial hypertension (see Clinical Considerations). Animal reproductive studies with treprostinil diolamine administered orally have shown an adverse effect on the fetus. In rats, administration of treprostinil to pregnant rats during the period of organogenesis at doses ≥10 mg/kg/day (approximately 15 times the human exposure at the dose of 3.5 mg BID on an AUC basis) resulted in decreased pregnancy rate, increased post-implantation loss, and decreased fetal viability and growth. In rabbits, teratogenicity and decreased fetal viability and growth were observed at doses ≥1.5 mg/kg/day (approximately 7 times the human exposure at the dose of 3.5 mg BID on an AUC basis) (see Animal Data).

The estimated background risk of major birth defects and miscarriage for the indicated populations is unknown. All pregnancies have a background risk of birth defect, loss, or other adverse outcomes. In the U.S. general population, the estimated background risk of major birth defects and miscarriage in clinically recognized pregnancies is 2 to 4% and 15 to 20%, respectively.

Section 42230-3 (42230-3)
This Patient Information has been approved by the U.S. Food and Drug Administration. Revised: 02/2023
Patient Information

Orenitram(®) (oh-REN-i-tram)

(treprostinil) extended-release tablets
What is Orenitram?
  • Orenitram is a prescription medicine used to treat pulmonary arterial hypertension (PAH) which is high blood pressure in the arteries of your lungs.
  • Orenitram can help slow down the progression of your disease and improve your ability to exercise.
It is not known if Orenitram is safe and effective in children.
Do not take Orenitram if you have severe liver problems.
Before taking Orenitram, tell your healthcare provider about all of your medical conditions, including if you:
  • have liver problems
  • have diverticulosis
  • are pregnant or plan to become pregnant. It is not known if Orenitram will harm your unborn baby.
  • are breastfeeding or plan to breastfeed. It is not known if Orenitram passes into your breast milk. Talk to your healthcare provider about the best way to feed your baby during treatment with Orenitram.
Tell your healthcare provider about all the medicines you take, including prescription and over-the-counter medicines, vitamins, and herbal supplements. Orenitram and other medicines may affect each other causing side effects. Do not start any new medicine until you check with your healthcare provider.

Especially tell your healthcare provider if you take another medicine that contains treprostinil, such as Remodulin®, Tyvaso®, or Tyvaso DPI®.
How should I take Orenitram?
  • Take Orenitram exactly as your healthcare provider tells you to take it.
  • Your healthcare provider will slowly increase your dose to find the dose of Orenitram that is right for you.
  • If you take the medicine Remodulin and your healthcare provider is switching you to Orenitram, your healthcare provider will decrease your dose of Remodulin over a period of time when you start taking Orenitram.
  • Do not change your dose or suddenly stop taking Orenitram without first talking to your healthcare provider.
  • Orenitram is usually taken 3 times a day (about every 8 hours) or 2 times a day (about every 12 hours). Your healthcare provider will tell you how often you should take Orenitram. If you have side effects, your healthcare provider may tell you to change your dose or when you take Orenitram.
  • Take Orenitram with food.
  • Swallow Orenitram tablets whole. Do not split, chew, crush, or break your Orenitram tablets. Do not take Orenitram tablets that are damaged or broken. If Orenitram tablets are not taken whole, they may release too much medicine at one time. This can lead to side effects.
  • You may see the tablet shell in your stools (bowel movements). This is usually normal. The tablet shell is not digested. If you have diverticulosis, the tablet shell may get stuck in a blind pouch or diverticulum in your intestine.
  • If you miss your dose of Orenitram, take the missed dose as soon as possible with food.
  • If you miss 2 or more doses of Orenitram, call your healthcare provider to see if you need to change your dose.
  • If you take too much Orenitram, call your healthcare provider or go to the nearest hospital emergency room right away.
What are the possible side effects of Orenitram?

Orenitram can cause serious side effects, including worsening of PAH symptoms.
  • Stopping Orenitram suddenly may cause worsening of your PAH symptoms. Do not change your dose or suddenly stop taking Orenitram without first talking to your healthcare provider.
The most common side effects of Orenitram include:
  • headache
  • diarrhea
  • nausea
  • vomiting
  • flushing
  • pain in arms and legs
  • jaw pain
Tell your healthcare provider if you have any side effect that bothers you or that does not go away.

These are not all of the possible side effects of Orenitram. For more information, ask your healthcare provider or pharmacist.

Call your healthcare provider for medical advice about side effects. You may report side effects to FDA at 1-800-FDA-1088.
How should I store Orenitram?
  • Store at 68°F to 77°F (20°C to 25°C).
Keep Orenitram and all medicines out of the reach of children.
General information about the safe and effective use of Orenitram.

Medicines are sometimes prescribed for purposes other than those listed in a Patient Information Leaflet.

Do not use Orenitram for a condition for which it was not prescribed. Do not give Orenitram to other people, even if they have the same symptoms that you have. It may harm them. You can ask your healthcare provider or pharmacist for information about Orenitram that is written for health professionals.
What are the ingredients in Orenitram?

Active ingredient: treprostinil diolamine

Inactive ingredients: xylitol, maltodextrin, sodium lauryl sulfate, magnesium stearate, cellulose acetate, triethyl citrate, polyvinyl alcohol, titanium dioxide, polyethylene glycol, and talc. In addition, tablets may contain colorants FD&C Blue #2, iron oxide yellow, and iron oxide red. The imprint ink contains shellac glaze, ethanol, isopropyl alcohol, iron oxide black, n-butyl alcohol, and propylene glycol.

United Therapeutics Corp., Research Triangle Park, NC 27709 USA

Copyright 2023, United Therapeutics Corp. All rights reserved.

ORENITRAM is a registered trademark of United Therapeutics Corp.

For more information, go to www.orenitram.com or call 1-877-864-8437.
Section 43683-2 (43683-2)
Dosage and Administration (2.1) 08/2023
16.2 Storage

Store at 20°C to 25°C (68°F to 77°F) with excursions permitted to 15°C to 30°C (59°F to 86°F) [See USP Controlled Room Temperature]. Keep out of reach of children.

10 Overdosage (10 OVERDOSAGE)

Signs and symptoms of overdose with Orenitram during clinical trials reflect its dose-limiting pharmacologic effects and include severe headache, nausea, vomiting, diarrhea, and hypotension. Treat supportively.

11 Description (11 DESCRIPTION)

Orenitram is an extended-release osmotic tablet for oral administration. Orenitram is formulated as the diolamine salt of treprostinil, a tricyclic benzindene analogue of prostacyclin. The chemical name is Acetic acid, 2-[[(1R,2R,3aS,9aS)-2,3,3a,4,9,9a-hexahydro-2-hydroxy-1-[(3S)-3-hydroxyoctyl]-1H-benz[f]inden-5-yl]oxy]-, complexed with 2,2'-iminobis[ethanol] (1:1). The molecular formula is C23H34O5∙C4H11NO2, the molecular weight is 495.65, and it has the following structural formula:

Orenitram tablets are formulated in five strengths, which contain 0.125 mg of treprostinil (equivalent to 0.159 mg treprostinil diolamine), 0.25 mg of treprostinil (equivalent to 0.317 mg treprostinil diolamine), 1 mg of treprostinil (equivalent to 1.27 mg treprostinil diolamine), 2.5 mg of treprostinil (equivalent to 3.17 mg treprostinil diolamine), or 5 mg of treprostinil (equivalent to 6.35 mg treprostinil diolamine). The formulations also contain xylitol, maltodextrin, sodium lauryl sulfate, magnesium stearate, cellulose acetate, triethyl citrate, polyvinyl alcohol, titanium dioxide, polyethylene glycol, and talc. In addition, tablets may contain colorants FD&C Blue #2, iron oxide yellow, and iron oxide red. The imprint ink contains shellac glaze, ethanol, isopropyl alcohol USP, iron oxide black, n-butyl alcohol, and propylene glycol.

Orenitram is designed to release treprostinil at a near zero-order rate using an osmotic tablet technology. The tablet core is coated with a semi-permeable membrane and has a laser-drilled aperture through the membrane. Upon contact with water (e.g., after ingestion), the core tablet absorbs water through the semi-permeable membrane. The water dissolves the water-soluble treprostinil diolamine and the water-soluble osmotic excipients, which creates hydrostatic pressure within the membrane, eventually forcing the drug across the membrane at a controlled rate.

16.1 How Supplied

Orenitram is an 8-mm round biconvex tablet with strength identified by color and print and supplied as follows:

Strength Color Printing on Tablets NDC #

100-Count Bottle
NDC #

10-Count Bottle
NDC #

10-Count Carton (Unit-Dose Blister)
0.125 mg White UT 0.125 66302-300-01 66302-300-10 66302-300-02
0.25 mg Green UT 0.25 66302-302-01 66302-302-10 66302-302-02
1 mg Yellow UT 1 66302-310-01 66302-310-10 66302-310-02
2.5 mg Pink UT 2.5 66302-325-01 66302-325-10 66302-325-02
5 mg Red UT 5 66302-350-01 66302-350-10 66302-350-02

Titration Kits for Orenitram are supplied in the following configurations:

Titration Kit Blister Configurations NDC #
Month 1 containing four weekly cartons Seven daily wallet blister packs in each weekly carton containing the following total number of tablets:
  • Week 1 (twenty-one × 0.125 mg tablets)
  • Week 2 (forty-two × 0.125 mg tablets)
  • Week 3 (twenty-one × 0.125 mg tablets and twenty-one × 0.25 mg tablets)
  • Week 4 (forty-two × 0.125 mg tablets and twenty-one × 0.25 mg tablets)
66302-361-28
Month 2 containing four weekly cartons Seven daily wallet blister packs in each weekly carton containing the following total number of tablets:
  • Week 5 (twenty-one × 0.125 mg tablets and forty-two × 0.25 mg tablets)
  • Week 6 (forty-two × 0.125 mg tablets and forty-two × 0.25 mg tablets)
  • Week 7 (twenty-one × 0.125 mg tablets and sixty-three × 0.25 mg tablets)
  • Week 8 (forty-two × 0.125 mg tablets and sixty-three × 0.25 mg tablets)
66302-362-56
Month 3 containing four weekly cartons Seven daily wallet blister packs in each weekly carton containing the following total number of tablets:
  • Week 9 (twenty-one × 0.125 mg tablets and twenty-one × 1 mg tablets)
  • Week 10 (forty-two × 0.125 mg tablets and twenty-one × 1 mg tablets)
  • Week 11 (twenty-one × 0.125 mg tablets, twenty-one × 0.25 mg tablets, and twenty-one × 1 mg tablets)
  • Week 12 (forty-two × 0.125 mg tablets, twenty-one × 0.25 mg tablets, and twenty-one × 1 mg tablets)
66302-363-84
8.4 Pediatric Use

Safety and effectiveness in pediatric patients have not been established.

8.5 Geriatric Use

Use of Orenitram in patients aged 65 years and over demonstrated slightly higher absolute and relative adverse event rates compared to younger patients. In general, dose selection for an elderly patient should be cautious, reflecting the greater frequency of decreased hepatic or cardiac function, and of concomitant disease or other drug therapy.

4 Contraindications (4 CONTRAINDICATIONS)

Severe hepatic impairment (Child Pugh Class C) [see Use In Specific Populations (8.6) and Clinical Pharmacology (12.3)].

6 Adverse Reactions (6 ADVERSE REACTIONS)

Most common adverse reactions (incidence >10%) reported in clinical studies in patients treated with Orenitram compared with placebo are headache, diarrhea, nausea, vomiting, jaw pain, and flushing. (6.1)



To report SUSPECTED ADVERSE REACTIONS, contact United Therapeutics Corp. at 1-866-458-6479 or FDA at 1-800-FDA-1088 or www.fda.gov/medwatch.

7 Drug Interactions (7 DRUG INTERACTIONS)
  • When co-administered with strong CYP2C8 inhibitors the initial dose is 0.125 mg BID with 0.125 mg BID dose increments not more frequently than every 3 to 4 days. (2.4, 7.1)
12.2 Pharmacodynamics

In a clinical trial of 240 healthy adult volunteers, single doses of inhaled treprostinil 54 µg (the target clinical dose) and 84 µg (supratherapeutic inhalation dose) prolonged the corrected QTc interval by approximately 10 msec. The QTc effect dissipated rapidly as the concentration of treprostinil decreased. Orenitram has not been evaluated in a thorough QTc study.

12.3 Pharmacokinetics

In patients with PAH, pharmacokinetics of treprostinil is dose-proportional for systemic exposure (AUC0-t) over the dose range from 0.5 to 15 mg BID. Upon repeat administration with a BID regimen, the accumulation in the systemic exposures to treprostinil is minimal and results in a peak-to-trough ratio of approximately 7. However, a TID regimen will reduce the peak-to-trough fluctuations to approximately 2.5 for the same total daily dose.

2.1 Recommended Dosing

Take Orenitram with food. Swallow Orenitram tablets whole; do not crush, split, or chew.

The recommended starting dose of Orenitram is 0.125 mg three times daily (TID) with food, taken approximately 8 hours apart or 0.25 mg twice daily (BID) with food, taken approximately 12 hours apart.

Titrate by 0.125 mg TID or 0.25 or 0.5 mg BID not more frequently than every 3 to 4 days. Increase the dose to the highest tolerated dose. The recommended maximum daily dose is 120 mg.

If dose increments are not tolerated, consider titrating slower. If intolerable pharmacologic effects occur, decrease the dose in increments of 0.125 mg TID or 0.25 mg BID. Avoid abrupt discontinuation [see Warnings and Precautions (5.1)].

1 Indications and Usage (1 INDICATIONS AND USAGE)

Orenitram is a prostacyclin mimetic indicated for the treatment of pulmonary arterial hypertension (PAH) (WHO Group 1):

  • To delay disease progression and to improve exercise capacity. The studies that established effectiveness included predominately patients with WHO functional class II-III symptoms and etiologies of idiopathic or heritable PAH (66%) or PAH associated with connective tissue disease (26%). (1.1)
12.1 Mechanism of Action

The major pharmacologic actions of treprostinil are direct vasodilation of pulmonary and systemic arterial vascular beds, inhibition of platelet aggregation, and inhibition of smooth muscle cell proliferation.

5 Warnings and Precautions (5 WARNINGS AND PRECAUTIONS)
  • Do not abruptly discontinue dosing. (2.5, 5.1)
  • In patients with diverticulosis, Orenitram tablets can become lodged in a diverticulum. (5.2)
2 Dosage and Administration (2 DOSAGE AND ADMINISTRATION)
  • Give with food. Swallow tablets whole; use only intact tablets. (2.1)
  • Starting dose: 0.125 mg TID or 0.25 mg BID. (2.1)
  • Titrate by 0.125 mg TID or by 0.25 mg or 0.5 mg BID, not more frequently than every 3 to 4 days as tolerated. The maximum daily dose is 120 mg. (2.1)
  • If transitioning from intravenous (IV) or subcutaneous (SC) Remodulin®, the Orenitram dose should be increased while simultaneously decreasing the IV/SC infusion rate. (2.2)
  • Mild hepatic impairment (Child Pugh Class A): Initiate at 0.125 mg BID. Increment at 0.125 mg BID not more frequently than every 3 to 4 days. (2.3)
  • Avoid use in patients with moderate hepatic impairment. (2.3)
3 Dosage Forms and Strengths (3 DOSAGE FORMS AND STRENGTHS)

Orenitram (treprostinil) extended-release tablets are available in the following five strengths:

  • -
    0.125 mg [White tablet imprinted with UT 0.125]
  • -
    0.25 mg [Green tablet imprinted with UT 0.25]
  • -
    1 mg [Yellow tablet imprinted with UT 1]
  • -
    2.5 mg [Pink tablet imprinted with UT 2.5]
  • -
    5 mg [Red tablet imprinted with UT 5]
6.2 Post Marketing Experience (6.2 Post-Marketing Experience)

The following adverse reactions have been identified during postapproval use of Orenitram: dizziness, dyspepsia, vomiting, myalgia, and arthralgia. Because these reactions are reported voluntarily from a population of uncertain size, it is not always possible to reliably estimate their frequency or establish a causal relationship to drug exposure.

6.1 Clinical Trials Experience

Because clinical trials are conducted under widely varying conditions, adverse reaction rates observed in the clinical trials of a drug cannot be directly compared to rates in the clinical trials of another drug and may not reflect the rates observed in clinical practice.

In a 12-week, placebo-controlled, monotherapy study (Study 1; WHO Group 1; functional class II-III), and an event-driven, placebo-controlled, combination therapy study (Study 4; WHO Group 1; functional class I-III), the most commonly reported adverse reactions that occurred in patients receiving Orenitram included: headache, diarrhea, nausea, and flushing.

Orenitram patients in Study 1 (N=151) had access to 0.25 mg tablets at randomization. Approximately 91% of such patients in Study 1 experienced an adverse reaction, but only 4% discontinued therapy for an adverse reaction (compared to 3% receiving placebo). Study 4 enrolled a total of 690 patients, 346 received Orenitram and 344 received placebo. Overall, 19% of patients treated with Orenitram discontinued treatment in Study 4 due to an adverse event (compared to 4% of patients receiving placebo). The exposure to Orenitram in Study 4 was up to 5.1 years with a median duration of exposure of 1.2 years. Table 1 summarizes adverse events with rates at least 5% higher on Orenitram therapy than on placebo that were reported in either Study 1 or 4.

Table 1: Adverse Events with Rates at Least 5% Higher on Orenitram Therapy than on Placebo in Either Study 1 or Study 4
Reaction Study 1

N=228
Includes all subjects in the Primary Analysis Population
Study 4

N=690
Orenitram

n=151
Placebo

n=77
Orenitram

n=346
Placebo

n=344
Headache 63% 19% 75% 35%
Diarrhea 30% 16% 69% 29%
Nausea 30% 18% 40% 23%
Vomiting 17% 16% 36% 10%
Flushing 15% 6% 45% 8%
Pain in jaw 11% 4% 18% 3%
Pain in extremity 14% 8% 18% 9%
Hypokalemia 9% 3% 4% 3%
Abdominal discomfort 6% 0% 8% 4%
Upper abdominal pain 5% 3% 12% 5%

Orenitram was studied in a long-term, open-label, extension study in which 824 patients were dosed for a mean duration of approximately 2 years. About 70% of patients continued treatment with Orenitram for at least a year. The mean dose was 4.2 mg BID at one year. The adverse reactions were similar to those observed in the placebo-controlled trials.

The safety of Orenitram was also evaluated in an open-label study transitioning patients from Remodulin. The safety profile during this study was similar to that observed in the three pivotal studies.

17 Patient Counseling Information (17 PATIENT COUNSELING INFORMATION)

See FDA-approved patient labeling (Patient Information).

Tell patients:

  • Abrupt discontinuation of therapy could result in worsening of PAH symptoms.
  • Take Orenitram with food.
  • Swallow Orenitram tablets whole. Do not split, chew, crush, or break. Do not take a tablet that is damaged or broken.
  • The biologically inert components of the tablet remain intact during gastrointestinal transit and are eliminated in the feces as an insoluble shell.
8.7 Patients With Renal Impairment (8.7 Patients with Renal Impairment)

No dose adjustments are required in patients with renal impairment. Orenitram is not removed by dialysis [see Clinical Pharmacology (12.3)].

1.1 Pulmonary Arterial Hypertension

Orenitram is indicated for the treatment of pulmonary arterial hypertension (PAH) (WHO Group 1) to delay disease progression and to improve exercise capacity.

The studies that established effectiveness included predominately patients with WHO functional class II-III symptoms and etiologies of idiopathic or heritable PAH (66%) or PAH associated with connective tissue disease (26%).

8.6 Patients With Hepatic Impairment (8.6 Patients with Hepatic Impairment)

There is a marked increase in the systemic exposure to treprostinil in hepatically impaired patients [see Dosage and Administration (2.3), Contraindications (4), and Clinical Pharmacology (12.3)].

2.5 Interruptions and Discontinuation

If a dose of medication is missed, the patient should take the missed dose as soon as possible, with food. If a patient misses two or more doses, restart at a lower dose and re-titrate.

In the event of a planned short-term treatment interruption for patients unable to take oral medications, consider a temporary infusion of subcutaneous or intravenous treprostinil. To calculate the total daily dose (mg) of treprostinil for the parenteral route use the following equation:

Remodulin (ng/kg/min) = 139 × Orenitram total daily dose (mg)
                      weight (kg)

When discontinuing Orenitram, reduce the dose in steps of 0.5 to 1 mg per day [see Warnings and Precautions (5.1)].

5.2 Use in Patients With Blind End Pouches (5.2 Use in Patients with Blind-end Pouches)

The tablet shell does not dissolve. In patients with diverticulosis, Orenitram tablets can lodge in a diverticulum.

7.1 Effect of Cyp2c8 Inhibitors On Treprostinil (7.1 Effect of CYP2C8 Inhibitors on Treprostinil)

Co-administration of Orenitram and the CYP2C8 enzyme inhibitor gemfibrozil in healthy adult volunteers increases exposure to treprostinil. Reduce the starting dose of Orenitram to 0.125 mg BID and use 0.125 mg BID increments not more frequently than every 3 to 4 days [see Dosage and Administration (2.4) and Clinical Pharmacology (12.3)].

5.1 Worsening Pah Symptoms Upon Abrupt Withdrawal (5.1 Worsening PAH Symptoms upon Abrupt Withdrawal)

Abrupt discontinuation or sudden large reductions in dosage of Orenitram may result in worsening of PAH symptoms.

2.4 Dose Adjustment for Use With Cyp2c8 Inhibitors (2.4 Dose Adjustment for Use with CYP2C8 Inhibitors)

When co-administered with strong CYP2C8 inhibitors (e.g., gemfibrozil) the initial dose is 0.125 mg BID with 0.125 mg BID dose increments not more frequently than every 3 to 4 days.

Principal Display Panel 1 Mg Tablet Bottle Label (PRINCIPAL DISPLAY PANEL - 1 mg Tablet Bottle Label)

NDC 66302-310-01

100 Tablets

Orenitram®

(treprostinil)

Extended-Release

Tablets

1 mg

Swallow whole.

Do not split, chew, crush,

or break tablets.

Principal Display Panel 5 Mg Tablet Bottle Label (PRINCIPAL DISPLAY PANEL - 5 mg Tablet Bottle Label)

NDC 66302-350-01

100 Tablets

Orenitram®

(treprostinil)

Extended-Release

Tablets

5 mg

Swallow whole.

Do not split, chew, crush,

or break tablets.

Principal Display Panel 2.5 Mg Tablet Bottle Label (PRINCIPAL DISPLAY PANEL - 2.5 mg Tablet Bottle Label)

NDC 66302-325-01

100 Tablets

Orenitram®

(treprostinil)

Extended-Release

Tablets

2.5 mg

Swallow whole.

Do not split, chew, crush,

or break tablets.

Principal Display Panel 0.25 Mg Tablet Bottle Label (PRINCIPAL DISPLAY PANEL - 0.25 mg Tablet Bottle Label)

NDC 66302-302-01

100 Tablets

Orenitram®

(treprostinil)

Extended-Release

Tablets

0.25 mg

Swallow whole.

Do not split, chew, crush,

or break tablets.

Principal Display Panel 0.125 Mg Tablet Bottle Label (PRINCIPAL DISPLAY PANEL - 0.125 mg Tablet Bottle Label)

NDC 66302-300-01

100 Tablets

Orenitram®

(treprostinil)

Extended-Release

Tablets

0.125 mg

Swallow whole.

Do not split, chew, crush,

or break tablets.

14.1 Clinical Trials in Pulmonary Arterial Hypertension

Four multicenter, randomized, double-blind studies were conducted and compared Orenitram to placebo in a total of 349 (Study 1), 350 (Study 2), 310 (Study 3), and 690 (Study 4) patients with PAH.

2.3 Dose Adjustment in Patients With Hepatic Impairment (2.3 Dose Adjustment in Patients with Hepatic Impairment)

In patients with mild hepatic impairment (Child Pugh Class A) start at 0.125 mg BID with 0.125 mg BID dose increments not more frequently than every 3 to 4 days. Avoid use of Orenitram in patients with moderate hepatic impairment (Child Pugh Class B). Orenitram is contraindicated in patients with severe hepatic impairment (Child Pugh Class C) due to increases in systemic exposure [see Contraindications (4), Use in Specific Populations (8.6), and Clinical Pharmacology (12.3)].

13.1 Carcinogenesis, Mutagenesis, Impairment of Fertility

Treprostinil diolamine did not demonstrate any carcinogenic effects in mouse or rat carcinogenicity studies. Oral administration of treprostinil diolamine to Tg.rasH2 mice at 0, 5, 10, and 20 mg/kg/day in males and 0, 3, 7.5, and 15 mg/kg/day in females daily for 26 weeks did not significantly increase the incidence of tumors. Oral administration of treprostinil diolamine to Sprague Dawley rats at 0, 1, 3, and 10 mg/kg/day daily for 104 weeks did not significantly increase the incidence of tumors. The exposures obtained at the highest dose levels used in males and females are about 13- and 18-fold, respectively, the human exposure at the dose of 3.5 mg BID on an AUC basis.

In vitro genotoxicity studies with high doses of treprostinil did not demonstrate any mutagenic or clastogenic effects. Treprostinil diolamine was tested in vivo in a rat micronucleus assay and did not induce an increased incidence of micronucleated polychromatic erythrocytes.

In rats, treatment with treprostinil diolamine had no effect on reproductive performance or sperm motility at doses up to 10 mg/kg/day. The exposures at this dose level are about 6- (male) to 11- (female) fold the human exposure at the dose of 3.5 mg BID on an AUC basis.

Principal Display Panel 1 Mg Tablet Blister Pack Carton (PRINCIPAL DISPLAY PANEL - 1 mg Tablet Blister Pack Carton)

Orenitram®

(treprostinil)

EXTENDED-RELEASE TABLETS

1 mg

per tablet

Swallow whole.

Do not split, chew,

crush, or break tablets.

10 Tablets

(1 x 10 tablet blister pack)

Pharmacist:

Dispense the accompanying Patient

Information Leaflet to each patient.

Rx Only

NDC 66302-310-02

Principal Display Panel 5 Mg Tablet Blister Pack Carton (PRINCIPAL DISPLAY PANEL - 5 mg Tablet Blister Pack Carton)

Orenitram®

(treprostinil)

EXTENDED-RELEASE TABLETS

5 mg

per tablet

Swallow whole.

Do not split, chew,

crush, or break tablets.

10 Tablets

(1 x 10 tablet blister pack)

Pharmacist:

Dispense the accompanying Patient

Information Leaflet to each patient.

Rx Only

NDC 66302-350-02

Principal Display Panel 2.5 Mg Tablet Blister Pack Carton (PRINCIPAL DISPLAY PANEL - 2.5 mg Tablet Blister Pack Carton)

Orenitram®

(treprostinil)

EXTENDED-RELEASE TABLETS

2.5 mg

per tablet

Swallow whole.

Do not split, chew,

crush, or break tablets.

10 Tablets

(1 x 10 tablet blister pack)

Pharmacist:

Dispense the accompanying Patient

Information Leaflet to each patient.

Rx Only

NDC 66302-325-02

Principal Display Panel 0.25 Mg Tablet Blister Pack Carton (PRINCIPAL DISPLAY PANEL - 0.25 mg Tablet Blister Pack Carton)

Orenitram®

(treprostinil)

EXTENDED-RELEASE TABLETS

0.25 mg

per tablet

Swallow whole.

Do not split, chew,

crush, or break tablets.

10 Tablets

(1 x 10 tablet blister pack)

Pharmacist:

Dispense the accompanying Patient

Information Leaflet to each patient.

Rx Only

NDC 66302-302-02

Principal Display Panel 0.125 Mg Tablet Blister Pack Carton (PRINCIPAL DISPLAY PANEL - 0.125 mg Tablet Blister Pack Carton)

Orenitram®

(treprostinil)

EXTENDED-RELEASE TABLETS

0.125 mg

per tablet

Swallow whole.

Do not split, chew,

crush, or break tablets.

10 Tablets

(1 x 10 tablet blister pack)

Pharmacist:

Dispense the accompanying Patient

Information Leaflet to each patient.

Rx Only

NDC 66302-300-02

Principal Display Panel 0.125 Mg 0.25 Mg Titration Kit Carton Month 1 (PRINCIPAL DISPLAY PANEL - 0.125 mg 0.25 mg Titration Kit Carton - Month 1)

Rx Only

NDC 66302-361-28

Orenitram®

(treprostinil)

EXTENDED-RELEASE TABLETS

Titration Kit

Month 1

0.125 mg

per tablet

0.25 mg

per tablet

Swallow whole.

Do not split, chew, crush, or break tablets.

Kit Contains:

168 tablets (126 x 0.125 mg per tablet and

42 x 0.25 mg per tablet).

Monthly carton contains 4 individual weekly cartons

each with 7 daily wallet blister packs.

Principal Display Panel 0.125 Mg 0.25 Mg Titration Kit Carton Month 2 (PRINCIPAL DISPLAY PANEL - 0.125 mg 0.25 mg Titration Kit Carton - Month 2)

Rx Only

NDC 66302-362-56

Orenitram®

(treprostinil)

EXTENDED-RELEASE TABLETS

Titration Kit

Month 2

0.125 mg

per tablet

0.25 mg

per tablet

Swallow whole.

Do not split, chew, crush, or break tablets.

Kit Contains:

336 tablets (126 x 0.125 mg per tablet and

210 x 0.25 mg per tablet).

Monthly carton contains 4 individual weekly cartons

each with 7 daily wallet blister packs.

Principal Display Panel 0.125 Mg 0.25 Mg 1 Mg Titration Kit Carton Month 3 (PRINCIPAL DISPLAY PANEL - 0.125 mg 0.25 mg 1 mg Titration Kit Carton - Month 3)

Rx Only

NDC 66302-363-84

Orenitram®

(treprostinil)

EXTENDED-RELEASE TABLETS

Titration Kit

Month 3

0.125 mg

per tablet

0.25 mg

per tablet

1 mg

per tablet

Swallow whole.

Do not split, chew, crush, or break tablets.

Kit Contains:

252 tablets (126 x 0.125 mg per tablet,

42 x 0.25 mg per tablet, and 84 × 1 mg per tablet).

Monthly carton contains 4 individual weekly cartons

each with 7 daily wallet blister packs.

2.2 Transitioning From Subcutaneous Or Intravenous Routes of Administration of Treprostinil (2.2 Transitioning from Subcutaneous or Intravenous Routes of Administration of Treprostinil)

Decrease the dose of Remodulin while simultaneously increasing the dose of Orenitram. The dose of Remodulin can be reduced up to 30 ng/kg/min per day and the dose of Orenitram simultaneously increased up to 6 mg per day (2 mg TID) if tolerated. The following equation can be used to estimate a target total daily dose of Orenitram in mg using a patient's dose of intravenous (IV)/subcutaneous (SC) treprostinil (in ng/kg/min) and weight (in kg).

Orenitram total daily dose (mg) = 0.0072 × Remodulin dose (ng/kg/min) × weight (kg)


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